Interbrachial Pinch by Trapezius Transfer in Amyoplasia Congenita: A Case Report
نویسندگان
چکیده
Amyoplasia congenita, or "classic distal arthrogryposis," is the most common disorder among the congenital, non-progressive, multiple joint contractural conditions named arthrogryposis. The cause remains unknown, and it occurs sporadically. Abnormal neurological examination indicates that movement in utero was diminished as a result of an abnormality of the central or peripheral nervous system, the motor end plate, or muscle. The absence of central neural pathology indicates the origin in akinetic fetal condition. Three weeks are enough to cause muscle weakness and joint fibrosis. Joint contractures in amyoplasia are often rigid and refractory to nonoperative treatment such as passive stretching. Surgery is focused on each patient's need respecting adaptive maneuvers to accomplish daily tasks. We present a case in which pectoral major muscle had no strength for pinching; a trapezius muscle transfer was planned to obtain an interbrachial pinch useful for grasping.
منابع مشابه
Amyoplasia Congenita of the Lower Extremity: Report in a Premature Baby
Amyoplasia congenita is a diagnostic subgroup of children with arthrogryposis multiplex congenita (AMC). AMC is a relatively rare syndrome characterized by multiple joint contractures at birth. Amyoplasia congenita is the most common type of this syndrome with an occurrence rate of 1 in 10,000 live births, and mainly refers to the disorders with limb involvement. In this report, the author pres...
متن کاملAmyoplasia Congenita Associated Wvith Mongolism
The rare condition known variously as multiple congenital articular rigidity, arthrogryposis multiplex congenita and amyoplasia congenita has been made known in this country mainly by the work of W. Sheldon9, who introduced the name used in this paper. A further title has been applied by D. S. Middleton', who uses the term myodystrophia foetalis deformans, as being more accurately descriptive o...
متن کاملAmyoplasia congenita associated with mongolism.
The rare condition known variously as multiple congenital articular rigidity, arthrogryposis multiplex congenita and amyoplasia congenita has been made known in this country mainly by the work of W. Sheldon9, who introduced the name used in this paper. A further title has been applied by D. S. Middleton', who uses the term myodystrophia foetalis deformans, as being more accurately descriptive o...
متن کاملAn Otogenic Trapezius Abscess: A Case Report
Introduction: An otogenic brain abscess is a common ENT problem but an otogenic trapezius abscess can also be experienced in otolaryngological practice, particularly in patients with chronic suppurative otitis media. Case Report: We report a rare case of a trapezius abscess in an eight-year-old girl who presented at the ENT, Head and Neck Surgery Postgraduate Medical Institute, Lady Readi...
متن کامل